Mucinous cystadenoma of the appendix: A Case Report

Dr. Amit Bhambri, Malhotra A, Jhobta R, Kaundal A, Pandey A K, Bhambri K, Juneja A

Dr. Amit Bhambri, Malhotra A, Jhobta R, Kaundal A, Pandey A K, Bhambri K, Juneja A

Keywords: Case Report, Appendiceal tumour, Mucinous cystadenoma, Mucinous cystadenocarcinoma

Abstract

Mucocoele of the appendix is a rare cystic dilatation of the appendiceal lumen caused by mucinous secretions and consecutive retention of mucus. It can be caused by either non-neoplastic or primary epithelial neoplastic disease.1,2 The neoplastic variants are caused by mucus-producing epithelial neoplasms including mucinous adenomas or cystadenomas, mucinous tumours of uncertain malignancy and mucinous cystadenocarcinomas. 2,3,5 Most of these tumours are asymptomatic and may be found incidentally.1,2,5,6,7 Others become symptomatic because of inflammation in, for example, acute appendicitis or as a cause of nonspecific abdominal pain,5 per rectal bleeding, ureteral obstruction, haematuria or intussusception.13 A major complication of neoplastic mucinous appendiceal tumours is the development of pseudomyxoma peritonei, which has a high rate of morbidity and mortality8.

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